2026-08-29_00000098|hard|29CP

Structural basis of autoantibody binding in IgLON5 disease; Electron microscopy 3.70Å
Protein #1 277 residues (65% resolved)

QSLEFNSPADNYTVCEGDNATLSCFIDEHVTRVAWLNRSNILYAGNDRWTSDPRVRLLINTPEEFSILITEVGLGDEGLYTCSFQTRHQPYTTQVYLIVHVPARIVNISSPVTVNEGGNVNLLCLAVGRPEPTVTWRQLRDGFTSEGEILEISDIQRGQAGEYECVTHNGVNSAPDSRRVLVTVNYPPTITDVTSARTALGRAALLRCEAMAVPPADFQWYKDDRLLSSGTAEGLKVQTERTRSMLLFANVSARHYGNYTCRAANRLGASSASMRLL

QSLEFNSPADNYTVCEGDNATLSCFIDEHVTRVAWLNRSNILYAGNDRWTSDPRVRLLINTPEEFSILITEVGLGDEGLYTCSFQTRHQPYTTQVYLIVHVPARIVNISSPVTVNEGGNVNLLCLAVGRPEPTVTWRQLRDGFTSEGEILEISDIQRGQAGEYECVTHNGVNSAPDSRRVLVTVNYPPTITDVTSARTALGRAALLRCEAMAVPPADFQWYKDDRLLSSGTAEGLKVQTERTRSMLLFANVSARHYGNYTCRAANRLGASSASMRLL
Protein #2 228 residues (100% resolved)

QLRLQESGPGLLKPSETLSLTCTVSGGSISDSNHYWGWIRQPPGKGLEWIGSIYFSGSTYYNPSLRSRVTISIATSNNQFSLRLPSLTAADTAVYYCARDVRRMFGATCFDYWGQGAVVTISSASTKGPSVFPLAPSSKSTSGGTAALGCLVKDYFPEPVTVSWNSGALTSGVHTFPAVLQSSGLYSLSSVVTVPSSSLGTQTYICNVNHKPSNTKVDKKVEPKSCDK

QLRLQESGPGLLKPSETLSLTCTVSGGSISDSNHYWGWIRQPPGKGLEWIGSIYFSGSTYYNPSLRSRVTISIATSNNQFSLRLPSLTAADTAVYYCARDVRRMFGATCFDYWGQGAVVTISSASTKGPSVFPLAPSSKSTSGGTAALGCLVKDYFPEPVTVSWNSGALTSGVHTFPAVLQSSGLYSLSSVVTVPSSSLGTQTYICNVNHKPSNTKVDKKVEPKSCDK
Protein #3 216 residues (100% resolved)

EIVLTQSPGTLSLSPGERATLSCRASQSVSSNYLAWYQQKPGQPPRLLIYGASSRAAGIADRFRGSGSGTDFTLTISRLEPEDFAVYLCQLYVTSQGYTFGPGTRVDVKRTVAAPSVFIFPPSDEQLKSGTASVVCLLNNFYPREAKVQWKVDNALQSGNSQESVTEQDSKDSTYSLSSTLTLSKADYEKHKVYACEVTHQGLRSPVTKSFNRGEC

EIVLTQSPGTLSLSPGERATLSCRASQSVSSNYLAWYQQKPGQPPRLLIYGASSRAAGIADRFRGSGSGTDFTLTISRLEPEDFAVYLCQLYVTSQGYTFGPGTRVDVKRTVAAPSVFIFPPSDEQLKSGTASVVCLLNNFYPREAKVQWKVDNALQSGNSQESVTEQDSKDSTYSLSSTLTLSKADYEKHKVYACEVTHQGLRSPVTKSFNRGEC
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Reference